Suspected idiopathic sclerosing orbital inflammation presenting as immunoglobulin G4-related disease: a case report
2011

Case Report of Suspected Idiopathic Sclerosing Orbital Inflammation

Sample size: 1 publication Evidence: low

Author Information

Author(s): Nagai Kazuki, Andoh Kazuo, Nakamura Noriko, Sakata Katsumi

Primary Institution: Nagai Clinic, Saiseikai Yokohama-shi Nanbu Hospital, Yokohama City University

Hypothesis

Is idiopathic sclerosing orbital inflammation related to immunoglobulin G4-related disease?

Conclusion

The case suggests that idiopathic sclerosing orbital inflammation may be associated with elevated serum immunoglobulin G4 levels.

Supporting Evidence

  • The patient's serum IgG4 levels were significantly elevated.
  • Symptoms improved after treatment with oral prednisolone.
  • Imaging studies indicated infiltration of fibrotic tissues in the orbit.

Takeaway

This study is about an 82-year-old woman with eye swelling and drooping, which was linked to a rare condition that might be related to a specific type of immune response.

Methodology

The patient was treated with oral prednisolone, and her symptoms and serum IgG4 levels were monitored over time.

Limitations

A biopsy could not be performed due to lack of patient consent, limiting definitive diagnosis.

Participant Demographics

An 82-year-old Japanese woman with a history of chronic thyroiditis.

Digital Object Identifier (DOI)

10.1186/1752-1947-5-427

Want to read the original?

Access the complete publication on the publisher's website

View Original Publication