Challenges in clinical and laboratory diagnosis of androgen insensitivity syndrome: a case report
2011

Challenges in Diagnosing Androgen Insensitivity Syndrome

Sample size: 1 publication Evidence: moderate

Author Information

Author(s): Melo Caroline OA, Silva Daniela M, da Cruz Aparecido D

Primary Institution: Pontifícia Universidade Católica de Goiás

Hypothesis

What is the extent of the mutation affecting the AR gene in a teenage girl with a male karyotype?

Conclusion

The case highlights the importance of accurate genetic testing for diagnosing androgen insensitivity syndrome.

Supporting Evidence

  • The patient had a male karyotype but was raised as a female.
  • Genetic testing revealed a large deletion in the AR gene.
  • Proper diagnosis is critical for appropriate gender assignment and treatment.

Takeaway

This study is about a girl who was raised as a girl but had a male chromosome pattern due to a genetic condition. It shows how important it is to do the right tests to understand such conditions.

Methodology

Genetic testing using PCR and FISH to identify mutations in the AR gene.

Limitations

FISH alone was insufficient for diagnosis due to the size of the probe used.

Participant Demographics

Caucasian female, aged 15.

Digital Object Identifier (DOI)

10.1186/1752-1947-5-446

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