Mice lacking caspase-2 are protected from behavioral changes, but not pathology, in the YAC128 model of Huntington disease
2011

Caspase-2 Deficiency Protects Mice from Behavioral Changes in Huntington's Disease

Sample size: 33 publication 10 minutes Evidence: moderate

Author Information

Author(s): Jeffrey B. Carroll, Amber L. Southwell, Rona K. Graham, Jason P. Lerch, Dagmar E. Ehrnhoefer, Li-Ping Cao, Wei-Ning Zhang, Yu Deng, Nagat Bissada, Mark R. Henkelman, Michael R. Hayden

Primary Institution: University of British Columbia

Hypothesis

Does the absence of caspase-2 affect the progression of Huntington's disease in mice?

Conclusion

Mice lacking caspase-2 show improved behavioral symptoms of Huntington's disease without changes in pathological features.

Supporting Evidence

  • Mice lacking caspase-2 performed at nearly wild-type levels on motor tasks.
  • Behavioral improvements were observed in cognitive flexibility tasks.
  • Pathological features such as striatal volume loss remained unchanged in caspase-2 deficient mice.

Takeaway

Mice without a specific protein called caspase-2 can move and think better when they have Huntington's disease, but their brains still get damaged.

Methodology

The study used YAC128 mice bred with caspase-2 deficient mice to assess behavioral and cognitive functions through various tasks.

Potential Biases

Potential bias in behavioral assessments due to the experimenter's knowledge of the genotypes.

Limitations

The study does not address the long-term effects of caspase-2 deficiency on overall health or other potential side effects.

Participant Demographics

Mice used were of the FVB/NJ strain, specifically bred for the study.

Statistical Information

P-Value

p = 0.0064

Statistical Significance

p<0.05

Digital Object Identifier (DOI)

10.1186/1750-1326-6-59

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