MODY-like diabetes associated with an apparently balanced translocation: possible involvement of MPP7 gene and cell polarity in the pathogenesis of diabetes
2009

MODY-like Diabetes Linked to a Balanced Translocation and MPP7 Gene

Sample size: 1 publication Evidence: low

Author Information

Author(s): Bhoj Elizabeth J, Romeo Stefano, Baroni Marco G, Bartov Guy, Schultz Roger A, Zinn Andrew R

Primary Institution: The University of Texas Southwestern Medical Center

Hypothesis

The translocation disrupted a diabetes gene.

Conclusion

The translocation and MODY-like diabetes in the proband could be coincidental, but MPP7 may play a role in islet cell dysfunction.

Supporting Evidence

  • The translocation did not disrupt known diabetes-related genes.
  • MPP7 is highly expressed in mouse pancreas and human islets.
  • The translocation breakpoints were mapped to high resolution.

Takeaway

A man with a specific type of diabetes had a genetic change that might be linked to a gene important for cell function, but it's not clear if they are connected.

Methodology

The study involved mapping translocation breakpoints and analyzing gene expression near these breakpoints.

Limitations

The study is based on a single case, limiting generalizability.

Participant Demographics

The proband was a 32-year-old Italian man.

Digital Object Identifier (DOI)

10.1186/1755-8166-2-5

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